Other than aortic stenosis, which conditions are associated with a bicuspid aortic valve? Type Recommendation Primary Congenital Acquired Bicuspid valve (2% prevalence - typically presents 4th to 6th decade) Congenital subaortic membrane Other congenital heart disease (e.g. supravalvular stenosis) Degenerative (senile) calcification - most common in the UK Rheumatic heart disease (usually associated with mitral valve disease) Systemic Lupus Erythematosus (SLE) Paget's disease Radiation Drugs
